Items for "neuronal ceroid lipofuscinoses"

Tripeptidyl-peptidase I in health and disease

The lysosomal lumen contains numerous acidic hydrolases involved in the degradation of carbohydrates, lipids, proteins, and nucleic acids, which are basic cell components that turn over continuously within the cell and/or are ingested from outside of the cell...

Keywords: autoactivation, glycosylation, lysosomal aminopeptidase, lysosomal storage disorder, neuronal ceroid lipofuscinoses, sedolisin